Study aid only. Verify against current guidelines, primary literature, staging manuals, and prescribing information before clinical use.

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Advanced Soft-Tissue Sarcoma — Systemic Therapy

First-line Second-line Later-line SECOND-LINE THIRD-LINE / LATER Advanced soft-tissue sarcoma by subtype & line Most subtypes Leiomyosarcoma / UPS Liposarcoma Leiomyosarcoma (later) Non-adipocytic Multiply refractory Anthracycline Doxorubicin ± ifosfamide EORTC 62012 ↗ Doublet Gemcitabine + docetaxel GeDDiS ↗ Adipocytic Trabectedin or eribulin liposarcoma-specific ↗ Alkylator Trabectedin vs dacarbazine ↗ TKI Pazopanib PALETTE ↗ Antiangiogenic Regorafenib REGOSARC ↗ Trial Clinical trial subtype-directed