Study aid only. Verify against current guidelines, primary literature, staging manuals, and prescribing information before clinical use.

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Thrombotic Thrombocytopenic Purpura (TTP) — Treatment

First-line Second-line SECOND-LINE Acquired TTP ADAMTS13 < 10% (immune) Acute episode Immunomodulation Relapse prevention Emergent Plasma exchange (PLEX) daily until recovery Immunosuppress Corticosteroids + PLEX Anti-VWF Caplacizumab HERCULES ↗ Anti-CD20 Rituximab frontline adjunct / relapse prevention ↗ Preemptive Rituximab for falling ADAMTS13 in remission ↗