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Immune Thrombocytopenia (ITP) — Treatment
First-line
Second-line
Later-line
SECOND-LINE
THIRD-LINE / LATER
Immune
thrombocytopenia
(newly diagnosed)
First-line
Second-line
Refractory
Standard
Corticosteroids
dexamethasone or prednisone
Rapid rise
IVIG (if bleeding)
+ steroids
TPO-RA
Eltrombopag / romiplostim / avatrombopag
thrombopoietin receptor agonist ↗
Anti-CD20
Rituximab
durable response in subset ↗
SYK
Fostamatinib
FIT trials ↗
Surgical
Splenectomy
durable remission ~60%
Combination
Immunosuppression / combination
individualized